Case 1: Congenital Femoral Deficiency, Type 1B

Pre-Op

Patient has congenital femoral deficiency (CFD) Type 1B on the right side. She presents with a shortened femur and hip deformities.

Predicted limb length discrepancy at skeletal maturity: 25 cm (~9.8 in.)

SUPERhip

In order to correct and realign the hip, Dr. Paley performed a SUPERhip procedure at age 2 years, 3 months, with internal fixation on her right side. Patient was in a spica cast for 6 months.

Patient after the SUPERhip procedure

 

First Lengthening

At age 3 years, 10 months, patient underwent first lengthening of the femur with external fixation (modular rail system). Fixator extended across the knee in order to protect the joint. Internal fixation was removed and an arthrogram performed on the right knee.

Follow Up - 6 Months

The new bone is consolidating.

Fixator Removal - 9 Months

Bone healing complete, total length gained: 8 cm. Fixator removed from femur and tibia. Dr. Paley inserts a rush rod and debrides bone and soft tissue.

Rush rod and remaining internal fixation removed 6 months later.

Second Lengthening

Patient has a 7.4 cm discrepancy. Second lengthening peformed at age 8 years, 2 months. Lengthening of her right femur performed with 8.5 mm internal PRECICE nail.

Patient currently undergoing second lengthening. Check back in the future for updates!

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